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中文名称： EHHADH抗原（重组蛋白）
英文名称： EHHADH Antigen (Recombinant Protein)
别 名： LBP; ECHD; LBFP; PBFE; L-PBE
储 存： 冷冻（-20℃）
相关类别： 抗原
概 述：
|
Fusion protein corresponding to a region derived from 283-572 amino acids of human EHHADH |
|
Full name: |
enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase |
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Synonyms: |
LBP; ECHD; LBFP; PBFE; L-PBE |
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Swissprot: |
Q08426 |
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Gene Accession: |
BC038948 |
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Purity: |
>85%, as determined by Coomassie blue stained SDS-PAGE |
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Expression system: |
Escherichia coli |
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Tags: |
His tag C-Terminus, GST tag N-Terminus |
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Background: |
The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene. |
