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中文名称：ACADS 抗原（重组蛋白）
英文名称： ACADS Antigen (Recombinant Protein)
别 名： Acyl-CoA dehydrogenase, C-2 to C-3 short chain; SCAD; ACAD3
储 存： 冷冻（-20℃）
相关类别： 抗原
概 述：
|
Fusion protein corresponding to C terminal 250 amino acids of human ACADS |
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Full name: |
Acyl-CoA dehydrogenase, C-2 to C-3 short chain |
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Synonyms: |
SCAD; ACAD3 |
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Swissprot: |
P16219 |
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Gene Accession: |
BC025963 |
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Purity: |
>85%, as determined by Coomassie blue stained SDS-PAGE |
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Expression system: |
Escherichia coli |
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Tags: |
His tag C-Terminus, GST tag N-Terminus |
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Background: |
This gene encodes a a tetrameric mitochondrial flavoprotein, which is a member of the acyl-CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Mutations in this gene have been associated with Short Chain Acyl-CoA Dehydrogenase Deficiency. It is an autosomal recessive disorder resulting in acute acidosis and muscle weakness in infants, and a form of lipid-storage myopathy in adults. |
