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  • Íÿ¹ALDH6A1¶à¿Ë¡¿¹Ìå

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ÖÐÎÄÃû³Æ£ºÍÿ¹ALDH6A1¶à¿Ë¡¿¹Ìå 

Ó¢ÎÄÃû³Æ£º Anti-ALDH6A1 rabbit polyclonal antibody

±ð      Ãû£º MMSDH; MMSADHA

Ïà¹ØÀà±ð£º Ò»¿¹

´¢      ´æ£º Àä¶³£¨-20¡æ£©

¿¹      Ô­£º ALDH6A1  

ËÞ      Ö÷£º Rabbit

·´Ó¦ÖÖÊô£º Human, Mouse, Rat

±ê ¼Ç Î Unconjugate

¿Ë¡ÀàÐÍ£º rabbit polyclonal

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Background:

This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.

Applications:

ELISA, WB, IHC

Name of antibody:

ALDH6A1

Immunogen:

Fusion protein of human ALDH6A1

Full name:

aldehyde dehydrogenase 6 family, member A1

Synonyms£º

MMSDH; MMSADHA

SwissProt:

Q02252

ELISA Recommended dilution:

2000-5000

IHC positive control:

Human thyroid cancer and human lung cancer

IHC Recommend dilution:

50-200

WB Predicted band size:

58 kDa

WB Positive control:

Rat kidney tissue

WB Recommended dilution:

500-2000





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