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021-54845833/15800441009
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Background: |
This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. |
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Applications: |
WB, IHC |
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Name of antibody: |
CLN6 |
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Immunogen: |
Synthesized peptide derived from internal of human CLN6. |
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Full name: |
ceroid-lipofuscinosis, neuronal 6, late infantile, variant |
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Synonyms： |
nclf; CLN4A; HsT18960 |
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SwissProt: |
Q9NWW5 |
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IHC positive control: |
Human cervix tissue |
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IHC Recommend dilution: |
50-100 |
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WB Predicted band size: |
36 kDa |
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WB Positive control: |
Hela cells lysate |
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WB Recommended dilution: |
500-3000 |
